Kaposi's sarcoma of skin

This code identifies a malignant vascular tumor, Kaposi's sarcoma, specifically when it manifests on the skin. It typically presents as purplish, red, or brown lesions that can be macules, papules, plaques, or nodules. This condition is often associated with human herpesvirus 8 (HHV-8) infection and is more common in immunocompromised individuals.

Apply this code when documentation clearly indicates a diagnosis of Kaposi's sarcoma affecting the integumentary system. This includes primary cutaneous lesions, regardless of their extent or location on the skin. Supporting documentation should include pathology reports confirming the diagnosis or physician notes explicitly stating "Kaposi's sarcoma of skin."

• Do not use this code for Kaposi's sarcoma affecting internal organs or lymph nodes; specific codes exist for those sites.
• Always code the underlying cause, such as HIV infection (B20), if documented as present and contributing to the Kaposi's sarcoma.
• Be mindful of laterality if specified in the documentation, though C46.0 does not differentiate left/right.