Mantle cell lymphoma, extranodal and solid organ sites

This code signifies a diagnosis of mantle cell lymphoma (MCL) that has originated or spread to sites outside of the lymph nodes, spleen, or bone marrow. It specifically indicates involvement of solid organs or other extranodal tissues. MCL is an aggressive B-cell non-Hodgkin lymphoma.

Apply this code when documentation confirms mantle cell lymphoma affecting organs such as the gastrointestinal tract, liver, lung, skin, or other non-lymphoid tissues. This diagnosis is typically established through biopsy and immunohistochemical staining.

• Ensure documentation clearly specifies "extranodal" involvement and the specific solid organ(s) affected.
• Do not use this code for nodal, splenic, or bone marrow involvement without extranodal disease.
• Sequence this code as the primary diagnosis when it is the reason for the encounter, or as a secondary diagnosis when it represents a co-morbidity.