Lymphoblastic (diffuse) lymphoma, intrathoracic lymph nodes

This code signifies a malignant neoplasm characterized by the uncontrolled proliferation of immature lymphoid cells, specifically affecting the lymph nodes located within the chest cavity. This aggressive form of non-Hodgkin lymphoma originates from precursor B or T lymphocytes.

Apply this code when documentation confirms a diagnosis of lymphoblastic lymphoma with primary involvement of intrathoracic lymph nodes, such as mediastinal or hilar lymph nodes. Supporting documentation must clearly specify the histological type as "lymphoblastic" and the anatomical site as "intrathoracic lymph nodes."

• Ensure the pathology report explicitly states "lymphoblastic lymphoma" and not another subtype of non-Hodgkin lymphoma.
• Verify that the affected lymph nodes are specifically identified as intrathoracic; involvement of extrathoracic sites would necessitate a different code.
• This code is for the primary diagnosis; any associated symptoms or complications should be coded additionally.