Lymphoblastic (diffuse) lymphoma, spleen

This code signifies a malignant neoplasm of the lymphatic system, specifically a type of non-Hodgkin lymphoma characterized by the proliferation of immature lymphoid cells (lymphoblasts), with primary involvement of the spleen. It represents an aggressive form of lymphoma originating in or extensively affecting the spleen.

Assign this code when documentation clearly indicates a diagnosis of lymphoblastic lymphoma with confirmed splenic involvement. This diagnosis is typically established through biopsy and histopathological examination of splenic tissue or imaging studies demonstrating significant splenic infiltration.

• Ensure the documentation specifies "lymphoblastic" and "spleen" to support this specific code.
• Do not use this code for other types of non-Hodgkin lymphoma affecting the spleen; verify the specific histological type.
• Code any associated symptoms or complications, such as splenomegaly, as secondary diagnoses.