Burkitt lymphoma, intrapelvic lymph nodes

This diagnosis code identifies a specific type of high-grade B-cell non-Hodgkin lymphoma, Burkitt lymphoma, when it originates in or primarily affects lymph nodes located within the pelvic cavity. This aggressive malignancy is characterized by rapid growth and often presents with bulky disease.

Apply this code when documentation explicitly states a diagnosis of Burkitt lymphoma and specifies involvement of intrapelvic lymph nodes. This includes primary pelvic involvement or metastatic spread to these nodes where the primary site is not otherwise specified or is also Burkitt lymphoma. Supporting documentation should include pathology reports confirming Burkitt lymphoma and imaging or clinical notes detailing pelvic lymph node involvement.

• Ensure the pathology report specifically identifies Burkitt lymphoma, not just "high-grade B-cell lymphoma, NOS."
• Verify the anatomical site is clearly documented as "intrapelvic lymph nodes" to differentiate from other lymph node sites.
• Do not use this code if the Burkitt lymphoma is documented in extranodal sites within the pelvis (e.g., ovary, bladder), as specific extranodal codes would be more appropriate.