Burkitt lymphoma, spleen

This code identifies a specific type of high-grade B-cell non-Hodgkin lymphoma, Burkitt lymphoma, when it primarily affects or involves the spleen. Burkitt lymphoma is characterized by rapid growth and aggressive behavior, often presenting with extranodal involvement.

Use this code when documentation explicitly states a diagnosis of Burkitt lymphoma with confirmed involvement of the spleen, either as the primary site or a significant site of metastasis. This code is appropriate when pathology reports confirm the diagnosis and imaging or clinical findings indicate splenic involvement.

• Ensure documentation clearly specifies "Burkitt lymphoma" and not another subtype of non-Hodgkin lymphoma.
• Verify splenic involvement is explicitly stated; do not assume based on generalized lymphoma.
• Consider sequencing with codes for other involved sites if documented, following ICD-10-CM guidelines for multiple primary or metastatic sites.