Enteropathy-type (intestinal) T-cell lymphoma not remission

This code represents a rare and aggressive form of non-Hodgkin lymphoma originating from T-cells in the small intestine, specifically when the disease has not responded to initial treatment or has recurred. It is characterized by malignant T-lymphocyte proliferation within the gastrointestinal tract, often associated with celiac disease.

Use this code for patients diagnosed with enteropathy-type T-cell lymphoma (EATL) who are currently undergoing treatment for active disease or have persistent disease after prior therapy. Documentation should clearly state the diagnosis of EATL and indicate that the patient has not achieved remission.

• Ensure documentation specifies "not having achieved remission" to differentiate from codes for EATL in remission.
• Do not confuse with other types of intestinal lymphoma or other T-cell lymphomas.
• Code any associated complications or symptoms, such as malabsorption or intestinal perforation, as secondary diagnoses.