Lymphangioma, any site

This code represents a benign malformation of the lymphatic system, characterized by dilated lymphatic channels that can occur anywhere in the body. These lesions are typically congenital but may become apparent later in life, presenting as soft, compressible masses. They result from abnormal development of lymphatic vessels, leading to fluid accumulation.

Use this code when documentation clearly identifies a patient with a lymphangioma, regardless of its anatomical location. This includes cystic hygromas, which are a common form of lymphangioma, and other lymphatic malformations. Supporting documentation should include pathology reports confirming the diagnosis or clinical notes describing a characteristic lesion identified as a lymphangioma.

• Do not confuse with hemangioma (D18.0-), which is a vascular malformation.
• If the lymphangioma is specified as malignant, a code from the C-series (e.g., C49.-) would be more appropriate.
• Always review documentation for specific site information, though this code is for "any site." If a more specific code exists for a particular site, consider its use if clinically appropriate and documented.