Desmoid tumor of unspecified site

This code represents a desmoid tumor, also known as an aggressive fibromatosis, occurring in an unspecified anatomical location. Desmoid tumors are rare, locally aggressive, non-metastasizing soft tissue neoplasms characterized by uncontrolled proliferation of fibroblasts and myofibroblasts. They can infiltrate surrounding tissues but do not spread to distant sites.

Use this code when documentation confirms a diagnosis of a desmoid tumor but the specific primary site (e.g., abdominal wall, extra-abdominal, intra-abdominal) is not clearly identified. This is appropriate for initial diagnosis when the location is still being investigated or when the documentation simply states "desmoid tumor" without further anatomical specificity.

• Avoid using this code if a more specific anatomical site for the desmoid tumor is documented; always strive for the highest level of specificity.
• Review pathology reports and imaging studies carefully for precise tumor location.
• Consider querying the provider if the site is unclear, as more specific codes (e.g., D48.111, D48.112) exist.