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ICD-10-CM D81 — Combined immunodeficiencies | Codelle

D81

ICD-10-CM

Combined immunodeficiencies

Clinical Notes

Excludes 1 — Not coded here

autosomal recessive agammaglobulinemia (Swiss type) (D80.0)

Code Hierarchy

Subcodes (10)

D81.0Severe combined immunodeficiency with reticular dysgenesis

D81.1Severe combined immunodeficiency w low T- and B-cell numbers

D81.2Severe combined immunodef w low or normal B-cell numbers

D81.3Adenosine deaminase [ADA] deficiency

D81.4Nezelof's syndrome

D81.5Purine nucleoside phosphorylase [PNP] deficiency

D81.6Major histocompatibility complex class I deficiency

D81.7Major histocompatibility complex class II deficiency

D81.8Other combined immunodeficiencies

D81.9Combined immunodeficiency, unspecified

Same Category

D81.0Severe combined immunodeficiency with reticular dysgenesis D81.1Severe combined immunodeficiency w low T- and B-cell numbers D81.2Severe combined immunodef w low or normal B-cell numbers D81.3Adenosine deaminase [ADA] deficiency D81.30Adenosine deaminase deficiency, unspecified D81.31Severe combined immunodef due to adenosine deaminase defic D81.32

Adenosine deaminase 2 deficiency

D81.39Other adenosine deaminase deficiency

D81.4Nezelof's syndrome

D81.5Purine nucleoside phosphorylase [PNP] deficiency

+5 more in this category