Autoimmune hypoparathyroidism

This code identifies a rare endocrine disorder where the body's immune system mistakenly attacks and damages the parathyroid glands, leading to insufficient production of parathyroid hormone (PTH). This deficiency results in hypocalcemia (low blood calcium) and hyperphosphatemia (high blood phosphate). It is a specific subtype of hypoparathyroidism with an autoimmune etiology.

Use this code when documentation explicitly states autoimmune hypoparathyroidism as the patient's diagnosis. This typically occurs in patients presenting with symptoms of hypocalcemia (e.g., tetany, paresthesias, seizures) and laboratory findings confirming low PTH, low calcium, and high phosphate, with further workup indicating an autoimmune cause (e.g., positive anti-parathyroid antibodies).

• Ensure documentation clearly specifies "autoimmune" as the cause of hypoparathyroidism; otherwise, a more general hypoparathyroidism code may be appropriate.
• Do not confuse with other forms of hypoparathyroidism, such as postsurgical or idiopathic, which have different ICD-10-CM codes.
• Code any associated manifestations of hypocalcemia (e.g., cataracts, basal ganglia calcification) separately, if documented.