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ICD-10-CM E88.4 — Mitochondrial metabolism disord… | Codelle

ICD-10-CM/E88/E88.4

E88.4

ICD-10-CM

Mitochondrial metabolism disorders

Clinical Notes

Excludes 1 — Not coded here

disorders of pyruvate metabolism (E74.4)
Kearns-Sayre syndrome (H49.81)
Leber's disease (H47.22)
Leigh's encephalopathy (G31.82)
Mitochondrial myopathy, NEC (G71.3)
Reye's syndrome (G93.7)

Code Hierarchy

▲E88Other and unspecified metabolic disorders

E88.4(current)

Subcodes (5)

E88.40Mitochondrial metabolism disorder, unspecified

E88.41MELAS syndrome

E88.42MERRF syndrome

E88.43Disorders of mitochondrial tRNA synthetases

E88.49Other mitochondrial metabolism disorders

Same Category

E88Other and unspecified metabolic disorders E88.0Disorders of plasma-protein metabolism, NEC E88.01Alpha-1-antitrypsin deficiency E88.02Plasminogen deficiency E88.09Oth disorders of plasma-protein metabolism, NEC E88.1

Lipodystrophy, not elsewhere classified

E88.10Lipodystrophy, unspecified

E88.11Partial lipodystrophy

E88.12Generalized lipodystrophy

E88.13Localized lipodystrophy

+5 more in this category