Corticobasal degeneration

This code represents corticobasal degeneration (CBD), a rare, progressive neurodegenerative disorder characterized by asymmetric motor dysfunction, including rigidity, dystonia, apraxia, and cortical sensory deficits. It is a tauopathy, meaning it involves abnormal tau protein accumulation in the brain, leading to neuronal damage and atrophy in specific cortical and basal ganglia regions.

Use this code when documentation explicitly states a diagnosis of corticobasal degeneration. This diagnosis is typically made by a neurologist based on a combination of clinical symptoms, neurological examination findings, and often supported by neuroimaging (e.g., MRI showing asymmetric cortical atrophy) or neuropathological confirmation.

• Ensure the documentation clearly distinguishes CBD from other atypical parkinsonian syndromes like progressive supranuclear palsy (PSP) or multiple system atrophy (MSA).
• Do not use this code for "corticobasal syndrome" (CBS) unless CBD is confirmed as the underlying etiology; CBS is a clinical presentation that can be caused by various pathologies.
• Sequence this code as the primary diagnosis when CBD is the reason for the encounter, and code any associated symptoms or complications separately.