Lennox-Gastaut syndrome, intractable, w status epilepticus

This code signifies a severe and rare form of childhood epilepsy, Lennox-Gastaut syndrome, which is characterized by multiple seizure types, intellectual disability, and a distinctive EEG pattern. The "intractable" designation indicates that the seizures are resistant to conventional antiepileptic drug therapy. The "with status epilepticus" component specifies a prolonged seizure or a series of seizures without full recovery of consciousness between them, representing a medical emergency.

Use this code when documentation clearly states a diagnosis of Lennox-Gastaut syndrome that is refractory to treatment and the patient is experiencing status epilepticus. This code is appropriate for inpatient admissions or emergency department encounters where status epilepticus is actively being managed in a patient with known intractable Lennox-Gastaut. Supporting documentation should include physician notes detailing seizure type, duration, treatment resistance, and the presence of status epilepticus.

• Ensure documentation explicitly states "intractable" and "status epilepticus" in conjunction with Lennox-Gastaut syndrome.
• Do not use this code if the Lennox-Gastaut syndrome is well-controlled or if status epilepticus is not present.
• Consider sequencing this code as the primary diagnosis if the status epilepticus is the reason for the encounter, followed by codes for any associated complications.