Dravet syndrome, intractable, with status epilepticus

This code represents Dravet syndrome, a severe form of epilepsy characterized by prolonged, frequent seizures that are difficult to control with medication. The "intractable" designation indicates that the seizures are refractory to standard treatment, and "with status epilepticus" specifies a life-threatening condition where seizures are continuous or occur without full recovery of consciousness between episodes.

Use this code when documentation clearly states a diagnosis of Dravet syndrome, explicitly noting that the seizures are intractable and the patient is currently experiencing or has recently experienced status epilepticus. This code is appropriate for inpatient or outpatient encounters where the management of this severe, ongoing seizure activity is the primary focus.

• Ensure documentation explicitly states "Dravet syndrome," "intractable," and "status epilepticus" to support this specific code.
• Do not use this code for other forms of intractable epilepsy without a confirmed diagnosis of Dravet syndrome.
• Sequence this code as the primary diagnosis when the intractable Dravet syndrome with status epilepticus is the reason for the encounter.