Other limb girdle muscular dystrophy

This code represents a group of inherited muscle disorders characterized by progressive weakness and wasting primarily affecting the proximal muscles of the shoulders and hips. These conditions are distinct from Duchenne or Becker muscular dystrophies and involve various genetic mutations leading to diverse clinical presentations.

Use this code when documentation specifies a diagnosis of limb-girdle muscular dystrophy (LGMD) that does not fit the criteria for specific, separately classified types (e.g., LGMD type 1A, 1B, 2A, etc.). This code is appropriate when the specific genetic subtype is unknown, or the documented LGMD falls into a less common or unclassified category.

• Ensure the physician documentation clearly states "other limb girdle muscular dystrophy" or a similar non-specific LGMD diagnosis.
• Avoid using this code if a more specific LGMD type (e.g., G71.01 for LGMD type 1A) is documented.
• Consider sequencing this code as the primary diagnosis when it is the reason for the encounter, followed by any associated symptoms or complications.