Angioid streaks of macula

This code describes angioid streaks specifically affecting the macula, which are irregular, crack-like dehiscences in Bruch's membrane of the retina. These streaks are typically bilateral and can lead to visual impairment due to choroidal neovascularization (CNV) or macular atrophy. They are often associated with systemic conditions like pseudoxanthoma elasticum (PXE), Paget's disease, or Ehlers-Danlos syndrome.

Use this code when documentation specifies angioid streaks with involvement of the macular region. This diagnosis is typically made during an ophthalmoscopic examination, often confirmed with fluorescein angiography or optical coherence tomography (OCT). Ensure the physician's notes clearly indicate the presence of angioid streaks and their localization to the macula.

• Always specify laterality (right, left, or bilateral) if documented.
• Code any underlying systemic conditions (e.g., PXE, Paget's disease) as primary diagnoses when applicable, with angioid streaks as a secondary diagnosis.
• Do not confuse with other macular degenerations or dystrophies; angioid streaks have a distinct etiology and appearance.