Pigmentary retinal dystrophy

This code describes a group of inherited eye disorders characterized by progressive degeneration of the photoreceptor cells in the retina, primarily the rods, leading to gradual vision loss. It typically manifests as night blindness, followed by peripheral vision constriction, and can eventually lead to central vision impairment.

Use this code when documentation specifies a diagnosis of pigmentary retinal dystrophy, including conditions like retinitis pigmentosa. This diagnosis is typically made based on ophthalmoscopic findings (e.g., bone-spicule pigmentation), electroretinography (ERG) results, and genetic testing.

• Differentiate from other retinal dystrophies that are not primarily pigmentary in nature.
• Specify laterality (right, left, or bilateral) if documented, using the appropriate subcategory.
• Ensure the medical record clearly supports the diagnosis with clinical findings and diagnostic test results.