Progressive external ophthalmoplegia, unspecified eye

This code describes a chronic, slowly progressive weakness of the extraocular muscles, leading to restricted eye movements. It is characterized by drooping eyelids (ptosis) and limited ability to move the eyes in various directions, often affecting both eyes symmetrically. The condition is typically a manifestation of mitochondrial disorders or other neuromuscular diseases.

This code is appropriate for documenting a diagnosis of progressive external ophthalmoplegia when the specific eye affected is not documented or is not relevant to the clinical presentation. It should be used when the physician's documentation clearly states "progressive external ophthalmoplegia" without further specification of laterality. Supporting documentation would include clinical notes detailing the characteristic eye movement limitations and ptosis.

• Only use this code when laterality is truly unspecified; otherwise, code to the specific eye (e.g., right, left, bilateral).
• Always look for documentation of the underlying cause, such as a mitochondrial myopathy, and code it as a primary or secondary diagnosis.
• Avoid using this code if the ophthalmoplegia is acute or due to a clearly identified, non-progressive cause (e.g., cranial nerve palsy).