Progressive external ophthalmoplegia, bilateral

This code describes a neurological disorder characterized by the gradual weakening and paralysis of the extraocular muscles, affecting both eyes. It results in impaired eye movement, often leading to ptosis and limited gaze in all directions. This condition is typically progressive and can be an isolated finding or part of a broader mitochondrial disorder.

Use this code when documentation clearly indicates a diagnosis of progressive external ophthalmoplegia affecting both eyes. This diagnosis is often supported by neurological examination findings demonstrating bilateral, slowly worsening restriction of eye movements, sometimes accompanied by ptosis. It is appropriate for cases where the condition is chronic and not due to an acute injury or infection.

• Ensure documentation specifies "progressive" and "bilateral" to support this specific code.
• Differentiate from acute or non-progressive ophthalmoplegia, which would require different codes.
• Consider coding any underlying systemic or mitochondrial disorders as primary diagnoses, if applicable, with this code as a secondary diagnosis.