Kearns-Sayre syndrome, left eye

This code identifies Kearns-Sayre syndrome affecting the left eye. Kearns-Sayre syndrome is a rare, progressive neuromuscular disorder characterized by external ophthalmoplegia, pigmentary retinopathy, and cardiac conduction defects, often with onset before age 20.

Use this code when documentation specifically indicates a diagnosis of Kearns-Sayre syndrome with involvement of the patient's left eye. This typically occurs in patients presenting with ptosis, limited eye movements, and visual impairment in the left eye, alongside other systemic features of the syndrome.

• Ensure the medical record clearly specifies "left eye" involvement for accurate laterality coding.
• Code additional manifestations of Kearns-Sayre syndrome, such as cardiac involvement (e.g., I45.81 for Brugada syndrome, if documented), separately.
• Do not confuse with other mitochondrial disorders or isolated ophthalmoplegia without the full syndrome criteria.