Argyll Robertson pupil, atypical

This code describes an Argyll Robertson pupil that does not fit the classic presentation associated with neurosyphilis. It is characterized by pupils that constrict poorly or not at all to light but constrict normally on accommodation (near vision). This atypical presentation suggests an underlying neurological condition other than syphilis.

Use this code when documentation specifies an Argyll Robertson pupil and explicitly states it is "atypical" or when syphilis has been ruled out as the etiology. This diagnosis is typically made during an ophthalmological or neurological examination. Supporting documentation should clearly distinguish it from the classic syphilitic form.

• Ensure documentation explicitly states "atypical" to differentiate from the classic syphilitic form.
• Review the patient's medical history for any indication of syphilis, as this would direct coding to A52.19.
• Do not code this with A52.19 (syphilitic Argyll Robertson pupil) due to the Excludes1 note.