Other rheumatic multiple valve diseases

This code signifies the presence of multiple heart valve disorders that are attributed to a rheumatic etiology, but do not fit into more specific categories of rheumatic multiple valve disease. It indicates a systemic inflammatory process affecting several heart valves simultaneously, leading to their dysfunction.

This code is appropriate when documentation specifies rheumatic involvement of more than one heart valve (e.g., mitral and aortic, or tricuspid and pulmonary) and a more precise combination code is not available. Use this code when the physician explicitly states "rheumatic multiple valve disease, not otherwise specified" or describes multiple rheumatic valvular lesions without a more specific diagnostic term.

• Ensure documentation clearly links the multiple valve involvement to a rheumatic origin.
• Do not use this code if a more specific combination code exists for the documented rheumatic multiple valve disease.
• Consider sequencing this code after any acute rheumatic fever codes (I00-I02) if the condition is active.