Other secondary pulmonary hypertension

This code signifies pulmonary hypertension that is a consequence of another underlying medical condition, rather than being idiopathic. It indicates elevated blood pressure within the pulmonary arteries due to a secondary cause, impacting the right side of the heart and lung circulation.

Use this code when documentation clearly states pulmonary hypertension is secondary to a specified condition, but the specific type of secondary pulmonary hypertension (e.g., due to left heart disease, lung disease, or chronic thromboembolism) is not further specified or does not have a more precise code. This code is appropriate when the etiology is known to be secondary, but the exact mechanism or specific secondary category is not detailed enough for a more specific code within the I27 category.

• Always sequence the underlying cause of the secondary pulmonary hypertension first, if known and documented.
• Avoid using this code if a more specific code for secondary pulmonary hypertension (e.g., I27.1, I27.20-I27.24) can be assigned based on documentation.
• Ensure the physician's documentation explicitly links the pulmonary hypertension to an underlying condition to support "secondary" coding.