Nonrheumatic pulmonary valve stenosis

This code identifies a narrowing of the pulmonary valve opening that is not caused by rheumatic fever. This congenital or acquired heart condition obstructs blood flow from the right ventricle to the pulmonary artery, increasing pressure within the right ventricle.

Apply this code when documentation specifies pulmonary valve stenosis and explicitly states or implies a non-rheumatic etiology. This is commonly seen in congenital heart disease or as a sequela of other non-rheumatic conditions affecting the valve. Supporting documentation includes echocardiogram reports detailing the stenosis and physician notes confirming the non-rheumatic origin.

• Differentiate carefully from rheumatic pulmonary valve stenosis (I06.0) based on physician documentation.
• Always look for documentation specifying the etiology; if rheumatic, a different code is required.
• Consider additional codes for associated congenital anomalies or heart failure if present and documented.