Endomyocardial (eosinophilic) disease

This diagnosis code represents a rare form of restrictive cardiomyopathy characterized by inflammation and fibrosis of the endocardium and inner myocardium. It often involves the apex and inflow tracts of the ventricles, leading to impaired diastolic filling and heart failure. The "eosinophilic" specifier indicates cases where eosinophil infiltration is a prominent feature.

Use this code for patients diagnosed with endomyocardial fibrosis or Loeffler's endocarditis. Documentation should clearly state the diagnosis of endomyocardial disease, with or without specific mention of eosinophilic involvement, based on biopsy, imaging (e.g., echocardiography, cardiac MRI), and clinical presentation.

• Differentiate from other types of cardiomyopathy; this code is specific to endomyocardial involvement.
• Ensure documentation specifies whether the condition is primary or secondary to another underlying disease (e.g., hypereosinophilic syndrome), as this may impact sequencing.
• Do not confuse with other restrictive cardiomyopathies like amyloidosis or sarcoidosis, which have distinct ICD-10-CM codes.