Lymphedema, not elsewhere classified

This code identifies swelling caused by an accumulation of lymph fluid due to a compromised lymphatic system. It represents primary lymphedema (congenital or inherited) or secondary lymphedema resulting from causes other than post-surgical removal of breast tissue. The condition typically manifests as chronic swelling in one or more limbs, but can affect other body parts.

Apply this code when documentation specifies lymphedema that is not explicitly linked to a mastectomy. This includes cases of primary lymphedema, or secondary lymphedema due to infection, trauma, radiation therapy (not for breast cancer), or other non-specified causes. Supporting documentation should clearly indicate the diagnosis of lymphedema and rule out a postmastectomy etiology.

• Do not use this code for lymphedema directly resulting from a mastectomy; refer to the Excludes1 note.
• Specify the affected limb(s) or body area when possible, though this code does not require laterality.
• Look for documentation of the underlying cause of the lymphedema, if known, to code it first if applicable.