Desquamative interstitial pneumonia

This code represents desquamative interstitial pneumonia (DIP), a rare form of idiopathic interstitial pneumonia characterized by the accumulation of macrophages in the alveolar spaces. It is a chronic, progressive lung disease that can lead to significant respiratory impairment.

Use this code when documentation clearly identifies a diagnosis of desquamative interstitial pneumonia. This diagnosis is typically established through lung biopsy findings showing characteristic macrophage accumulation and often supported by clinical presentation and imaging studies.

• Ensure the physician's documentation explicitly states "desquamative interstitial pneumonia" to support this specific code.
• Differentiate from other idiopathic interstitial pneumonias (e.g., usual interstitial pneumonia, non-specific interstitial pneumonia) based on biopsy results.
• Code any associated symptoms or complications, such as respiratory failure, separately.