Peliosis hepatis

This code represents peliosis hepatis, a rare, non-neoplastic vascular condition characterized by multiple, blood-filled cystic spaces within the liver parenchyma. These spaces are typically lined by endothelial cells and can vary in size, potentially leading to hepatomegaly, liver dysfunction, or spontaneous rupture.

Use this code when documentation explicitly states a diagnosis of peliosis hepatis, often identified through imaging studies such as CT, MRI, or ultrasound, or confirmed by liver biopsy. This diagnosis may be encountered in patients with chronic debilitating diseases, those on long-term corticosteroid therapy, or individuals with certain infections.

• Ensure documentation clearly distinguishes peliosis hepatis from other cystic liver lesions or hemangiomas.
• Code any underlying conditions or causative factors (e.g., specific medications, infections) separately.
• If liver failure or hemorrhage is present due to peliosis hepatis, code these complications in addition to the primary diagnosis.