Pemphigus foliaceous

Pemphigus foliaceous is a chronic autoimmune blistering disease characterized by superficial blistering and erosions primarily affecting the skin, often sparing mucous membranes. It results from autoantibodies targeting desmoglein 1, leading to acantholysis in the superficial epidermis.

This code is used for patients diagnosed with pemphigus foliaceous, a specific subtype of pemphigus. Documentation should clearly state the diagnosis of pemphigus foliaceous, often supported by biopsy findings showing superficial acantholysis and direct immunofluorescence demonstrating intercellular IgG deposition in the epidermis.

• Differentiate from other pemphigus subtypes (e.g., pemphigus vulgaris) which have distinct codes.
• Ensure documentation specifies "foliaceous" to justify this specific code.
• Consider additional codes for any associated complications or manifestations, such as secondary infections (e.g., L08.9).