Bullous pemphigoid

This code represents an autoimmune blistering skin disorder characterized by the formation of large, tense blisters on an erythematous or normal-appearing base. It typically affects older adults and is caused by autoantibodies targeting components of the dermal-epidermal junction. The condition often presents with severe itching and can involve widespread skin surfaces.

Use this code for patients diagnosed with bullous pemphigoid, confirmed by clinical presentation, histopathology (subepidermal blister with eosinophils), and direct immunofluorescence (linear C3 and IgG deposition at the basement membrane zone). This diagnosis is appropriate when the physician's documentation clearly identifies this specific autoimmune blistering disease.

• Differentiate from other blistering disorders like pemphigus vulgaris or dermatitis herpetiformis, which have distinct ICD-10-CM codes.
• Ensure documentation specifies "bullous pemphigoid" and not a more general term like "blistering skin disease."
• Consider additional codes for any associated complications, such as secondary infections of the bullae.