Juvenile rheu arthritis w systemic onset, multiple sites

This code signifies a chronic inflammatory autoimmune disease affecting children, characterized by arthritis in multiple joints accompanied by systemic features such as fever, rash, lymphadenopathy, hepatosplenomegaly, and serositis. It represents the most severe subtype of juvenile idiopathic arthritis, impacting various organ systems beyond the joints.

Assign this code when documentation clearly indicates a diagnosis of juvenile rheumatoid arthritis with systemic onset, and the arthritis affects more than one joint. Supporting documentation should detail the systemic manifestations alongside the polyarticular involvement.

• Ensure the documentation explicitly states "systemic onset" and "multiple sites" to differentiate from other JIA subtypes.
• Do not confuse with other forms of juvenile idiopathic arthritis that lack systemic features or are pauciarticular.
• Review for any associated complications or manifestations that may require additional coding.