Sjogren syndrome with central nervous system involvement

This code represents Sjögren syndrome, a chronic autoimmune disorder characterized by dry eyes and mouth, when it affects the central nervous system (CNS). CNS involvement can manifest as a wide range of neurological symptoms, including cognitive dysfunction, seizures, myelopathy, or optic neuritis.

Use this code when a patient with a confirmed diagnosis of Sjögren syndrome presents with documented neurological signs or symptoms directly attributable to the underlying autoimmune disease. Documentation should clearly link the CNS manifestations to Sjögren syndrome, often supported by imaging, CSF analysis, or neurological examination findings.

• Always sequence the Sjögren syndrome code first, followed by codes for specific neurological manifestations if applicable.
• Distinguish from Sjögren syndrome without CNS involvement (M35.00) or with other organ involvement (e.g., M35.01 for lung involvement).
• Ensure the medical record explicitly states the connection between Sjögren syndrome and the CNS symptoms, rather than just listing co-occurring conditions.