Nephrotic syndrome with C3 glomerulonephritis

This code represents nephrotic syndrome occurring concurrently with C3 glomerulonephritis, a specific immune-mediated kidney disease characterized by abnormal complement protein deposition. Patients typically present with significant proteinuria, hypoalbuminemia, edema, and hyperlipidemia, alongside histological evidence of C3 glomerulonephritis.

Use this code when documentation explicitly states a diagnosis of nephrotic syndrome and C3 glomerulonephritis. This typically follows a kidney biopsy confirming C3 glomerulonephritis in a patient exhibiting the classic signs and symptoms of nephrotic syndrome.

• Ensure documentation clearly differentiates C3 glomerulonephritis from other forms of glomerulonephritis.
• Do not code this with N04.6 (Nephrotic syndrome with dense deposit disease) as per the Excludes1 note.
• Confirm the presence of all components of nephrotic syndrome (proteinuria, hypoalbuminemia, edema, hyperlipidemia) in the medical record.