Heredit nephrop, NEC w focal and seg glomerular lesions

This code describes a genetic kidney disorder characterized by inherited abnormalities in kidney structure and function, specifically affecting the glomeruli. The condition presents with focal and segmental scarring or damage within these filtering units of the kidney, leading to proteinuria and progressive renal dysfunction. It encompasses various hereditary nephropathies that do not fit into more specific categories.

Use this code when documentation indicates a diagnosis of hereditary nephropathy where the specific genetic cause is either unknown or not classifiable to a more precise code, and renal biopsy findings confirm focal and segmental glomerular lesions. This code is appropriate for patients with a family history of kidney disease and histological evidence of this particular glomerular pathology.

• Ensure documentation explicitly states "hereditary nephropathy" and "focal and segmental glomerular lesions."
• Do not use this code if a more specific hereditary nephropathy (e.g., Alport syndrome, Fabry disease) is identified and has its own distinct ICD-10-CM code.
• Code any associated chronic kidney disease (CKD) stage as a secondary diagnosis to fully capture the patient's renal status.