Neonatal diabetes mellitus

This code signifies a rare form of diabetes that manifests in the first six months of life, characterized by hyperglycemia requiring insulin or other glucose-lowering interventions. It results from genetic defects affecting pancreatic beta-cell function, leading to insufficient insulin production.

Apply this code when documentation confirms a diagnosis of diabetes mellitus presenting within the neonatal period (birth to 28 days) or early infancy (up to 6 months of age). Supporting documentation should include laboratory findings of elevated blood glucose and clinical signs consistent with diabetes.

• Differentiate from transient neonatal diabetes, which often resolves spontaneously.
• Do not confuse with gestational diabetes affecting the mother, or type 1 diabetes with later onset.
• Always sequence this code as the primary diagnosis if it is the reason for the encounter.