Malformations of aqueduct of Sylvius

This code describes congenital structural abnormalities affecting the cerebral aqueduct, also known as the aqueduct of Sylvius. These malformations can lead to obstruction of cerebrospinal fluid (CSF) flow, often resulting in hydrocephalus. The condition is present at birth and may manifest with varying degrees of severity.

Assign this code when documentation specifies a congenital malformation, stenosis, or atresia of the aqueduct of Sylvius. This diagnosis is typically supported by imaging studies such as MRI or CT scans of the brain, demonstrating the anatomical anomaly and often associated ventricular dilation.

• Always confirm the congenital nature of the aqueduct malformation; acquired stenosis would be coded differently.
• Code any associated hydrocephalus separately, as it is a common consequence but not inherent to the malformation itself.
• Review documentation for specific details regarding the type of malformation (e.g., stenosis, atresia) to ensure accurate coding.