Other congenital lens malformations

This code signifies a congenital anomaly of the crystalline lens that does not fit into more specific categories such as congenital cataract, aphakia, or subluxation. It encompasses a range of less common developmental defects affecting the lens structure, shape, or position from birth. These malformations can impact visual acuity and may require ophthalmologic intervention.

Assign this code when documentation specifies a congenital lens malformation that is not a cataract, aphakia, or luxation/subluxation. Examples include microphakia, spherophakia, lenticonus, or lentiglobus when explicitly stated as congenital. Supporting documentation should clearly identify the lens anomaly as present at birth or of developmental origin.

• Do not use this code for acquired lens conditions or for congenital cataracts (Q12.0) or congenital aphakia (Q12.3).
• Ensure the documentation specifies "congenital" or "developmental" to differentiate from acquired lens abnormalities.
• Consider sequencing this code after any associated visual impairment or other ocular anomalies if they are the primary reason for the encounter.