Macrotia

This code represents a congenital anomaly characterized by abnormally large ears. It is a developmental malformation where the auricle (external ear) is disproportionately larger than average for the individual's age and body size. This condition can affect one or both ears.

Use this code when documentation clearly indicates a diagnosis of abnormally large ears present at birth or identified early in life. It is appropriate for reporting the primary diagnosis in cases of isolated macrotia or as a secondary diagnosis when macrotia is part of a broader syndrome. Supporting documentation should include a physician's diagnostic statement.

• Ensure the documentation specifies "macrotia" or "abnormally large ears" rather than general ear size concerns.
• Distinguish from acquired ear enlargement, which would not be coded here.
• If macrotia is part of a recognized syndrome, code the syndrome first, followed by this code as a secondary diagnosis.