Superior sinus venosus atrial septal defect

This code describes a congenital heart defect where there is an abnormal opening in the atrial septum, specifically located near the superior vena cava (SVC) entrance. This defect is often associated with anomalous pulmonary venous return, where one or more right pulmonary veins drain into the SVC or right atrium instead of the left atrium. This results in a left-to-right shunt, increasing blood flow to the right side of the heart and lungs.

Use this code when documentation clearly indicates a diagnosis of a superior sinus venosus atrial septal defect. This diagnosis is typically made through echocardiography, cardiac catheterization, or surgical findings. Look for explicit mention of the defect's location near the SVC and any associated anomalous pulmonary venous return.

• Differentiate from other types of atrial septal defects (e.g., ostium secundum, ostium primum) based on anatomical location.
• Code any associated anomalous pulmonary venous return separately if specified, as it is a common co-occurrence.
• Ensure the documentation specifies "superior sinus venosus" to accurately assign this specific code.