Other congenital malformations of aortic and mitral valves

This code signifies congenital structural defects affecting both the aortic and mitral heart valves that are not classified elsewhere. These malformations are present at birth and can include a range of anomalies such as hypoplasia, dysplastic leaflets, or abnormal valve attachments impacting blood flow.

Apply this code when documentation specifies a congenital malformation involving both the aortic and mitral valves that does not have a more specific ICD-10-CM code. This is appropriate for conditions like congenital bicuspid aortic valve with concurrent mitral valve prolapse, or other unspecified congenital anomalies affecting both valves.

• Ensure documentation clearly states the congenital nature of the malformation and involvement of both the aortic and mitral valves.
• Avoid using this code if a more specific congenital anomaly code exists for the documented condition (e.g., Q23.0 for congenital aortic valve stenosis).
• Consider sequencing with codes for associated cardiac conditions or symptoms, such as heart failure (I50.-) or arrhythmias (I47-I49), if present.