Arteriovenous malformation of vessel of upper limb

This code signifies a congenital anomaly characterized by an abnormal tangle of arteries and veins in the upper extremity, bypassing the capillary system. This direct connection results in high-pressure arterial blood flowing into low-pressure veins, potentially leading to vessel dilation, rupture, or ischemia of surrounding tissues.

Apply this code when documentation explicitly identifies an arteriovenous malformation (AVM) located in any vessel of the arm, forearm, or hand. Supporting documentation should include diagnostic imaging (e.g., angiography, MRI, CT scan) confirming the presence and location of the AVM.

• Ensure the documentation specifies the upper limb; AVMs in other locations require different codes.
• Do not confuse with acquired fistulas, which are coded differently.
• Sequence as a primary diagnosis when the AVM is the reason for the encounter, or as a secondary diagnosis if it's a co-morbidity impacting treatment.