Agenesis and underdevelopment of nose

This code signifies the congenital absence or incomplete formation of the nose. This can range from a complete lack of nasal structures (agenesis) to a significantly underdeveloped nose (hypoplasia), affecting both external and internal nasal components.

Assign this code for congenital malformations where the nose is either entirely absent or abnormally small and underdeveloped at birth. Documentation should clearly state "agenesis of nose," "nasal aplasia," or "hypoplastic nose" as a congenital anomaly.

• Differentiate from acquired nasal deformities or trauma; this code is strictly for congenital conditions.
• Do not use for minor cosmetic nasal variations or septal deviations unless explicitly documented as part of a hypoplastic condition.
• Consider additional codes for associated congenital anomalies, especially those affecting the face or respiratory system, as these often co-occur.