Congenital tracheo-esophageal fistula without atresia

This code describes a birth defect where an abnormal connection exists between the trachea and the esophagus, but the esophagus itself is not completely closed off. This allows food or liquids to pass from the esophagus into the airway, or air from the trachea into the esophagus. Infants often present with coughing, choking, and respiratory distress during feeding.

Use this code for documented cases of congenital tracheo-esophageal fistula where there is no esophageal atresia. This diagnosis is typically made postnatally based on clinical signs and confirmed by imaging studies such as esophagram or bronchoscopy. Documentation should clearly state the presence of a fistula and the absence of esophageal atresia.

• Differentiate carefully from tracheo-esophageal fistula with atresia, which is a distinct and more severe condition.
• Ensure documentation explicitly states "without atresia" or provides clinical details confirming the esophagus is patent.
• Consider additional codes for associated congenital anomalies or complications, such as aspiration pneumonia.