Other congenital malformations of liver

This code signifies a congenital structural abnormality of the liver that does not fit into more specific categories of congenital liver malformations. These can include various developmental anomalies present at birth, such as accessory lobes, atypical lobulations, or other structural variations. It excludes conditions like biliary atresia, Caroli's disease, or congenital cysts of the liver.

Use this code when documentation specifies a congenital malformation of the liver that is not otherwise classified or specifically coded elsewhere in ICD-10-CM. This applies to cases where imaging studies (e.g., ultrasound, CT, MRI) or surgical findings identify an unusual liver morphology present from birth. Documentation should clearly state the congenital nature of the malformation and rule out acquired conditions.

• Ensure the documentation explicitly states the malformation is "congenital" and not an acquired condition or injury.
• Review for more specific congenital liver malformation codes (e.g., Q44.0-Q44.6) before defaulting to this "other" code.
• Avoid using this code for functional liver disorders or acquired liver diseases; it is strictly for structural birth defects.