Agenesis, aplasia and hypoplasia of pancreas

This code signifies the congenital absence, incomplete development, or underdevelopment of the pancreas. This can range from a complete lack of pancreatic tissue (agenesis) to a smaller-than-normal pancreas with reduced exocrine and/or endocrine function (hypoplasia). These conditions often lead to severe malabsorption and diabetes mellitus from birth.

Use this code for newborns or infants diagnosed with a congenital malformation involving the pancreas's formation. Documentation should clearly state agenesis, aplasia, or hypoplasia of the pancreas, typically confirmed by imaging studies (e.g., ultrasound, MRI) and clinical presentation of pancreatic insufficiency.

• Differentiate between congenital absence/underdevelopment and acquired pancreatic atrophy or destruction.
• Code any associated conditions, such as diabetes mellitus (E10.-) or malabsorption (K90.-), as secondary diagnoses.
• Ensure documentation specifies the congenital nature of the pancreatic anomaly.