Congenital absence of ovary, unilateral

This code signifies the complete absence of one ovary from birth. It is a rare congenital anomaly where ovarian tissue fails to develop on one side of the pelvis. This condition can impact reproductive potential and hormonal balance.

Apply this code when documentation clearly states a congenital, unilateral absence of an ovary. This diagnosis is typically made through imaging studies (e.g., ultrasound, MRI) and/or surgical exploration. Use this code for patients presenting with primary amenorrhea or infertility investigations revealing this specific anatomical defect.

• Ensure documentation specifies "congenital" and "unilateral" to differentiate from acquired conditions or bilateral absence.
• Do not confuse with ovarian agenesis (Q50.00) if laterality is specified.
• Consider sequencing with codes for associated conditions or symptoms, such as primary amenorrhea (N91.0).