Agenesis and aplasia of cervix

This code represents the congenital absence or incomplete development of the uterine cervix. This anomaly can occur in isolation or as part of more complex Müllerian duct anomalies, impacting reproductive function and menstrual flow. Patients may present with primary amenorrhea or cyclic pelvic pain due to hematometra if a uterus is present.

Use this code for documented cases of congenital absence or aplasia of the cervix, confirmed by imaging studies such as MRI or ultrasound, or during surgical exploration. It is appropriate when the patient's medical record clearly indicates the congenital nature of the cervical malformation.

• Differentiate from acquired cervical stenosis or atresia, which are coded differently.
• Always review documentation for associated anomalies of the uterus, vagina, or kidneys, and code them separately if present.
• Ensure the physician's notes explicitly state "agenesis" or "aplasia" of the cervix to support this specific code.