Congenital vasocutaneous fistula

This code represents a rare congenital anomaly characterized by an abnormal connection between a blood vessel (artery or vein) and the skin. This fistula is present at birth and can manifest as a visible lesion, often with pulsatile or palpable characteristics. It signifies a developmental defect in vascular formation.

Use this code when documentation clearly indicates a congenital abnormal communication between a blood vessel and the skin. This typically involves a physician's diagnosis of a congenital vasocutaneous fistula. Supporting documentation should specify the congenital nature of the vascular anomaly.

• Ensure documentation explicitly states "congenital" to differentiate from acquired fistulas.
• Do not use for acquired arteriovenous fistulas (e.g., traumatic or iatrogenic); these have different code assignments.
• Code any associated symptoms or complications, such as hemorrhage or infection, as secondary diagnoses.