Congenital hydronephrosis

This code signifies a congenital malformation characterized by the dilation of the renal pelvis and calyces due to an obstruction of urine flow, present at birth. This condition can affect one or both kidneys and may lead to impaired renal function if not managed.

Use this code for diagnoses of hydronephrosis explicitly documented as congenital in origin, often identified prenatally or in infancy. Documentation should clearly state the congenital nature of the hydronephrosis, distinguishing it from acquired forms.

• Ensure documentation specifies "congenital" to differentiate from acquired hydronephrosis (N13.30-N13.39).
• Code any associated congenital anomalies of the kidney and urinary tract (CAKUT) separately.
• Consider laterality if specified in the documentation (e.g., Q62.00 for unspecified, Q62.01 for unilateral, Q62.02 for bilateral).